Congenital haemolytic anaemia associated with abnormal inducible red cell cation permeability.

نویسندگان

R M Gardiner

N D Barnes

J C Ellory

چکیده

Congenital haemolytic anaemia in a 14 year old girl was caused by increased red cell membrane cation permeability. Potassium permeability was unusually sensitive to hydrostatic pressure and treatment with N-ethylmaleimide, factors which activate a specific chloride dependent potassium channel in cell membranes.

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